MyPACS.net: Radiology Teaching Files > Case 32888337

previously visited 091027 BRONCHOGENIC CYST WITH CONGENITAL LOBAR EMPHYSEMA
Contributed by: pedrad CSH, Radiologist, Chung Shan Medical University Hospital, Taiwan.
Patient: 5 day old male
History:

Chief complain:
Dyspnea and short of breath for 2 days.
Blood oxygen saturation: 70%

Birth history
Normal spontaneous delivery with gestational age 39+4 weeks.
Caesarean section due to cephlopelvic disproportion with prolonged labor
Birthbody weight: 3320gm.
Apgar score: 9 (at 1st min) to 10 (at 5th min).
Polyhydramnios was noted at about 20wks of gestational age.
Recovery was noted in follow-up.

Images:[small]larger

Fig. 1: Plain film radiography

Fig. 2: CT_cor

Fig. 3: CT_sag

Fig. 4: CT_axi

Fig. 5: CT_MinIP_cor

Fig. 6: CT_axi_colored

Fig. 7: CT_3D volume rendering

Fig. 8: MR_T2 weighted echo train spin echo with iterative decomposition of water and fat with echo asymmetry and least-squares estimation_cor

Fig. 9: MR_T2 weighted echo train spin echo with fat saturation_axi

Fig. 10: MR_T1 weighted echo train spin echo with fat saturation (left) and with intravenous gadolinium-enhanced image (right)_chest

Fig. 11: MR_T1 weighted echo train spin echo with fat saturation (left) and with intravenous gadolinium-enhanced image (right)_neck
Findings:

Plain film radiography (figure 1):

1. Left side deviation of mediastinum.
2. Decreased opacity of the right lung compared to left lung.


Multidetector row CT scan of chest with intravenous contrast, and
 with multiplanar reconstruction, maximum-intensity projection,
 minimum-intensity projection, 3D volume rendering, and colored
 multiplanar reconstruction (figure 2-7):

1. Relative hyperinflation of right upper lobe lung and lateral
   segment of right middle lobe lung with distended alveoli and
   decreased caliber of its vessels, suggesting congenital lobar
   emphysema (figure 2-7).
   Presence of mass effect of above lesion with compression of
   adjacent right lower lobe lung and left side deviation of
   mediastinum.
2. Poor demonstration of right upper lobe bronchus, possibly
   associated with stenosis/obstruction (figure 5).
   Some alveolar densities in medial part of right upper lobe
   lung with some atelectasis, may due to infectious/inflammatory
   process.
3. A 1.2cm well-defined ovoid lower density lesion without
   significant contrast enhancement in right suprahilar region
   (figure 2-4), nature to be determined.
   Another 0.9cm lower density lesion with mass effect in right
   lateral neck (figure 2,3), behind right lobe of thyroid gland with
   unknown etiology.
4. No abnormal finding in left lung.


1.5 Tesla MRI of neck and chest with T2 weighted echo train spin echo
 with fat saturation, T1 weighted echo train spin echo with fat
 saturation, diffusion-weighted echo-planar MR imaging,
 T1 weighted Dixon fat-water chemical shift gradient echo,
 T2 weighted echo train spin echo with iterative decomposition of
 water and fat with echo asymmetry and least-squares estimation,
 and with intravenous gadolinium-enhanced images (figure 8-11):

1. A 1.2cm well-defined ovoid long T1 and T2 cystic lesion without
   significant restricted water diffusibility or contrast enhancement
   in right suprahilar region of mediastinum (figure 8-10), nature to
   be determined.
   Bronchogenic cyst may be considered firstly.
2. Another 0.9cm lesion with similar MR signals in right
   lateral neck, behind right lobe of thyroid gland (figure 8,9,11).
3. History of congenital lobar emphysema.
   Presence of relative hyperinflation of right upper and middle
   lobe lung with decreased vascular density.
   Left side deviation of mediastinum.


Pathology (excision of mediastinal cystic lesion):
A cystic lesion with respiratory lining and lymphoid tissue,
 consisted with broncogenic cyst (not showed).

Diagnosis: Bronchogenic cyst with congenital lobar emphysema
Comments:
No comments posted.
Additional Details:

Case Number: 32888337Last Updated: 11-17-2009
Anatomy: Chest   Pathology: Benign Mass, Cyst
Modality: CT, Conventional Radiograph, MR, 3D ReconstructionAccess Level: Readable by all users
Keywords: bronchogenic, emphysemaACR: 674.3156

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